Informasjon

Langerhans-celle histiocytose

Histiocytose er en sjelden sykdom som skyldes overskudd av en type hvite blodceller kalt histiocytter. Histiocyttene klumper seg sammen og kan angripe hud, bein, lever, milt, tannkjøtt, lunger, øyne, ører og/eller sentralnervesystemet.

Årsak

Vi kjenner ikke årsaken, men det dreier seg om en forstyrrelse i immunapparatet. Om det er en svulst eller om det er en betennelse, vet vi altså ikke sikkert i dag. Dersom det er en svulst, tyder mye på at det er en ganske godartet svulsttype.

Dette dokumentet er basert på det profesjonelle dokumentet "Langerhans-celle histiocytose". Referanselisten for dette dokumentet vises nedenfor.

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